Abstract: Objective To investigate the behavioral problems in Williams syndrome children and provide basis for forepart psychology intervene. Methods From August 2011 to December 2012,applying Conners Parents Symptom Questionnaire,17 cases of Williams Syndromes children and 25 normal children were compaired to assess behavioral problems. Results Comparing to normal children,the incidence of behavioral problems were significantly higher in WS children,and scores of each scale were higher than normal children with significant difference(P<0.05);but no difference between the different ages(3-8Y、9-14Y) and genders. Conclusion Williams syndrome children often accompanied by a variety of behavioral problems,attention deficit hyperactivity disorder is the most common.The incidence of behavioral problems does not increased with age.

Key words: Williams syndrome, behavioral problems, Conners Parents Symptom Questionnaire

摘要： 目的 探讨我国Williams综合征儿童的心理行为问题,为早期干预提供依据。方法 在2011年8月-2012年12月期间,采用Conners父母症状问卷(Parent Symptom Questionaire,PSQ),对17例Williams综合征(Williams syndrome,WS)及25例正常儿童进行对照研究,评估其各种行为问题。结果 Williams综合征儿童行为问题的发生率明显高于正常儿童;WS组各种行为问题的症状评分值均高于正常儿童(P<0.05);但在不同年龄段(3~8岁、9~14岁)及不同性别之间差异均无统计学意义(P>0.05)。结论 WS儿童常合并存在各种心理行为问题,以注意缺陷多动障碍最为常见,随着年龄增长其发生率无明显升高。

关键词: Williams综合症, 心理行为问题, Conners父母症状问卷