【Objective】 To acknowledge the health care status and demands of children born with birth defects. 【Methods】 Between July 2007 and September 2008, 453 live born cases of birth defects were diagnosed and registered by the Beijing Birth Defects Monitoring network-a hospital based birth defects registry system. Their parents were called to assess their survival status from birth up to the age of 6~8 months. 【Results】 The proportions of 315 live born infants with birth defects inhabited in Beijing, Expanded Program of Immunization, and physical examination were 94.00%, 93.40% respectively. The proportions of having been to the hospital once at least, not having been to the hospital, not acknowledging the fact of infants' birth defects were 70.70%, 27.10%, and 2.20% respectively. 【Conclusions】 The medical services were not enough for the demands of children born with birth defects. To establish registry system of children born with birth defects, to accomplish the net of diagnosis, therapy and transport of children born with birth defect will provide more services to the children born with birth defects.